June 2015
Volume 56, Issue 7
Free
ARVO Annual Meeting Abstract  |   June 2015
Visual outcomes after vitreoretinal surgery in Wagner-Stickler Syndrome retinal detachment
Author Affiliations & Notes
  • Giuliano Stramare
    Ospedale Sacro Cuore- Negrar - Verona, Negrar - VR, Italy
  • Footnotes
    Commercial Relationships Giuliano Stramare, None
  • Footnotes
    Support None
Investigative Ophthalmology & Visual Science June 2015, Vol.56, 5089. doi:
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      Giuliano Stramare; Visual outcomes after vitreoretinal surgery in Wagner-Stickler Syndrome retinal detachment. Invest. Ophthalmol. Vis. Sci. 2015;56(7 ):5089.

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      © ARVO (1962-2015); The Authors (2016-present)

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Abstract

Purpose: The Wagner-Stickler syndrome is a hereditary progressive arthro-ophthalmopathy with an autosomal dominant pattern of inheritance. Both conditions involve varying degrees of degeneration of eye structures including myopia, presenile cataracts, strabismus, vitreo-retinal degeneration and rhegmatogenous retinal detachments. Only the Stickler syndrome has been associated with other variable non ocular symptoms such as deafness and facial, oral and skeletal abnormalities. <br /> OBJECTIVE: To study the outcome of the treatment of retinal detachment in Wagner-Stickler patients.<br />

Methods: Retrospective analysis of 14 patients (19 eyes) with retinal detachments. Mean visual acuity was 0,90 logMar. Mean age was 7,29. Mean refractive errors was -12 sph. Mean follow up is 5,46 years. All the eyes were managed with 20G vitrectomy.

Results: Five eyes devoloped proliferative vitreoretinopathy and was re-operated and the retina remained attached. Three eyes developed an ocular hypertension well managed with topical beta blocker therapy. <br /> One eyes had a central corneal opacity.<br /> Mean visual acuity after surgery was 0,50 logMar.<br />

Conclusions: Wagner-Stickler Syndrome retinal detachment is often complex in nature. Vitrectomy is effective in the repair of retinal detachment and can improve visual outcomes.

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