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A. Agarwal; Corrugations of the RPE in Juvenile X– Linked Macular Retinoschisis . Invest. Ophthalmol. Vis. Sci. 2006;47(13):2793.
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To describe a peculiar "Sea Gull" like corrugations of the retinal pigment epithelium (RPE) in 2 siblings with juvenile X– linked retinoschisis.
Two siblings aged 10 and 18 at the time of their initial evaluation underwent clinical examination, fluorescein angiography and optical coherence tomography (OCT). The fundus appearance was correlated with the angiographic and OCT findings.
Both brothers presented with typical macular schisis. The OCT demonstrated cyst like spaces at the level of the outer plexiform layer and within the photoreceptor layer. Peculiar hitherto undescribed corrugations were seen temporal to the macula in both eyes of each patient. Fluorescein angiogram and OCT through these corrugations confirm their location to be at the level of the RPE.
Whether forces generated by the progressive enlargement of the macular schisis imparts localized folds in the RPE temporal to it.
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