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R.S. Wirthlin, C.W. Mango, A. Gupta, C.R. Gonzales, J. Perloff, S.D. Schwartz; Retinopathy in Adult Patients With Congenital Heart Disease . Invest. Ophthalmol. Vis. Sci. 2006;47(13):5173.
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To determine the presence of retinal vascular disease and vascular anomalies in an adult population of patients with congenital heart disease (CHD).
IRB–approved, prospective consecutive case series of four adult patients with congenital heart disease examined by a single observer at one institution. Wide–angle Optos® photography to document retinopathy.
Four patients were examined. Patient One was a 30 year–old woman with coarctation of the aorta, malposition of great arteries, double inlet single left ventricle status post 4 cardiac surgeries. Most recent surgery was 12 years prior to presentation. Visual acuity (VA) measured 20/20 OU. There were no ocular abnormalities. Patient Two was a 42 year–old man with non–restrictive ventricular septal defect, Eisenmenger syndrome, situs inversus, dextrocardia. VA measured 20/20 OD and 20/30 OS. There was evidence of retinal vascular tortuosity. Patient Three was a 37 year–old woman with coarctation of the aorta status post repair times two, most recently 6 years prior to presentation. VA measured 20/20 OU. There was evidence of retinal vascular tortuosity. Patient Four was a 61 year–old man with coarctation of the aorta 39 years status post repair. VA measured 20/20 OU. There was evidence retinal vascular tortuosity, arterial narrowing and arterial–venous crossing changes. 3 of 4 patients showed evidence of retinal vascular tortuosity.
Adult patients with CHD status post repair may have retinal vascular abnormalities. In adult patients with retinal vascular tortuosity, CHD should be considered.
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