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Devasis Reddy, Yoshihiro Yonekawa, Benjamin J Thomas, Eric Nudleman, George A. Williams; Long-term surgical outcomes of retinal detachment in patients with Stickler syndrome. Invest. Ophthalmol. Vis. Sci. 2016;57(12):1051.
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© 2017 Association for Research in Vision and Ophthalmology.
To present the long-term anatomic and visual outcomes of retinal detachment repair in patients with Stickler syndrome.
We conducted a retrospective, single-center, interventional, consecutive case series of patients with Stickler syndrome who underwent retinal reattachment surgery at our institution and seen between 2009 and 2014.
Sixteen eyes from 13 patients (mean age 10.5 years) were identified. Patients underwent on average 3.1 surgeries (range 1-13), and had 94 months (range 5-313) of post-operative follow-up. Twelve (75%) eyes developed proliferative vitreoretinopathy. All eyes eventually had successful reattachment with 10 eyes (63%) requiring silicone oil at last follow-up. Mean visual acuity before surgery was 20/914 (1.66 LogMar), and 20/796 (1.60 LogMar) at final follow-up (P = 0.81). There was a correlation between presenting and final visual acuity (P < 0.001). Patients with worse presenting visual acuities were more likely to require silicone oil tamponade at last examination (P = 0.04). In 6 of 13 patients (46%) there was bilateral retinal pathology seen during the study period. 4 of these patients developed bilateral retinal detachment, and 2 of these patients developed retinal tears in the fellow eyes. Seven fellow eyes were treated with prophylactic 360 degree laser photocoagulation. The average duration of time between retinal detachment in the presenting eye and tears or detachments in the fellow eye was 2 months (range 0-10).
Retinal detachment repair in patients with Stickler syndrome usually requires multiple surgeries to achieve reattachment. In our series, all retinal detachments were successfully reattached, but visual outcomes were variable, and correlated with presenting visual acuity.
This is an abstract that was submitted for the 2016 ARVO Annual Meeting, held in Seattle, Wash., May 1-5, 2016.
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