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HARRY A. QUIGLEY, MORTON F. GOLDBERG; Conjunctival Ultrastructure in Mucolipidosis III (Pseudo-Hurler Polydystrophy). Invest. Ophthalmol. Vis. Sci. 1971;10(8):568-580.
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Conjunctival biopsies from two sibs with mucolipidosis III and from their clinically normal parents were examined by histochemistry and electron microscopy. Connective tissue cells were filled with single membrane-limited vacuoles which frequently contained membranous lamellar material. These findings indicate abnormal mucopolysaccharide and glycolipid accumulation in this disorder and suggest a mechanism for the corneal clouding in these patients.
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