Abstract
Purpose: :
To describe the clinical aspects of three cases with acute idiopathic polymorphous vitelliform maculopathy (AIPVM) with special emphasis on the OCT findings.
Methods: :
Clinical records of three cases of AIPVM were used to analyse the clinical presentation of this rare disorder and compared to literature.
Results: :
The following data were evaluated: Prodromal complaints / visual acuity / dark adaptation / electrophysiology (ERG / EOG) / FA / ICG / color fundusphotographe, and OCT. We had the opportunity to perform close follow–up of one patient with the OCT in the active stage. Two patients were no longer in the active stage of the disease, and provided information about the end–stage of the disorder.
Conclusions: :
The three patients fiited in the definition of the disease as first described by Gass in 1988. OCT findings showed an extensive foveal neurosensory detachment, with an atypical posterior border, despite normal visual acuity. Two patients with long follow–up showed the disease to be self–limited, but in one patient visual acuity progressively deteriorated due to atrophy of the macula.
Keywords: macula/fovea • imaging/image analysis: clinical • retinal degenerations: hereditary