Abstract
Abstract: :
Purpose:Microphthalmia with cyst is a rare condition whereby a posterior cystic structure develops secondary to the proliferation of neuroectoderm through a closure defect in the embryonic optic fissure. Visual potential is limited secondary to optic nerve dysfunction plus maldevelopment of other structures including the cornea, anterior segment and retina. Methods:We report the amblyopic treatment and surgical correction of a 3-year-old with unilateral microphthalmos with cyst and esotropia. Results:At birth the patient had non-recordable visual evoked potentials (VEP) in the affected eye. With correction of hyperopic anisometropia, patching, and surgical correction of a 50 prism diopter esotropia, the visual acuity developed to 20/160 at 5 inches and ocular alignment to within 10 prism diopters of midline Conclusions:Visual acuity and strabismic alignment can be improved in children with appropriate amblyopic treatment and surgical alignment.
Keywords: strabismus: etiology • amblyopia • strabismus: treatment