Investigative Ophthalmology & Visual Science Cover Image for Volume 65, Issue 7
June 2024
Volume 65, Issue 7
Open Access
ARVO Annual Meeting Abstract  |   June 2024
Identification and characterization of a novel mouse model for age-associated retinal degeneration
Author Affiliations & Notes
  • Olivia J. Marola
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Michael MacLean
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Travis Cossette
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Cory Diemler
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Alaina Reagan
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Amanda A. Hewes
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Gareth R Howell
    The Jackson Laboratory, Bar Harbor, Maine, United States
  • Footnotes
    Commercial Relationships   Olivia Marola None; Michael MacLean None; Travis Cossette None; Cory Diemler None; Alaina Reagan None; Amanda Hewes None; Gareth Howell None
  • Footnotes
    Support  None
Investigative Ophthalmology & Visual Science June 2024, Vol.65, 729. doi:
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      Olivia J. Marola, Michael MacLean, Travis Cossette, Cory Diemler, Alaina Reagan, Amanda A. Hewes, Gareth R Howell; Identification and characterization of a novel mouse model for age-associated retinal degeneration. Invest. Ophthalmol. Vis. Sci. 2024;65(7):729.

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      © ARVO (1962-2015); The Authors (2016-present)

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Abstract

Purpose : Age is a primary risk factor for prominent retinopathies like glaucoma and age-related macular degeneration. Susceptibility to age-related retinal neurodegeneration is likely genetically influenced. To better understand and model age-related retinopathies, molecular aging signatures were identified in an array of 9 diverse mouse strains. Among these, wild-derived WSB/EiJ (WSB) mice exhibited a distinct aging signature indicating pronounced photoreceptor loss. Here, we longitudinally characterized retinal aging in WSB mice to assess their utility in modeling age-related photoreceptor degeneration.

Methods : RNA-sequencing and proteomics were employed to profile retinal aging signatures in an array of genetic backgrounds, including pigmented, wild-derived, and albino mouse strains at 4, 12, and 18M. Subsequently, WSB and B6 mice were subjected to a battery of longitudinal in vivo examinations (n≥18 eyes, both sexes) at 4, 8, 12, and 18M, including fundus exams, optical coherence tomography (OCT), and electroretinograms (ERG). Retinal morphological assessment was performed ex vivo at 4 and 18M (H&E, n≥12 eyes, both sexes). Data were analyzed with two-way ANOVAs with Sidak post-hoc tests and are listed as %difference±SEM where appropriate.

Results : Multi-omic analyses revealed WSB mice lose photoreceptor-associated transcripts and proteins with age. Fundus exams showed instances of pigmentary loss in WSB retinas (11% at 12M and 36% at 18M; not evident in B6). OCT measurements indicated WSB retinas were 21.9±0.6% thinner than B6 retinas at 4M (p<0.001). B6 retinas had subtle age-related thinning from 4-18M (4.5±0.8%, p=0.021), however, WSB retinas had significantly more age-related thinning (21.4±2.0%, p<0.001), most notably of the outer nuclear layer (ONL; 45.7±3.0%, p<0.001). Histology confirmed degenerated or absent ONLs at 18M, particularly in the central retina. WSB ERG a-wave, b-wave, and oscillatory potential amplitudes were significantly lower than B6 at 4M (47.2±5.7, 59.2±2.5, and 80.2±1.6% respectively, p<0.001), and WSB a-waves declined from 4-18M (53.2±2.6%, p<0.001).

Conclusions : Here, we provide a multi-omic resource of retinal aging across diverse mice, which can aid in understanding retinal aging and disease. This database identified WSB mice as a potentially novel model of photoreceptor degeneration, which was substantiated and characterized via OCT, H&E, and ERG analyses.

This abstract was presented at the 2024 ARVO Annual Meeting, held in Seattle, WA, May 5-9, 2024.

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